A Case of Acquired Zonal Aganglionosis in Adult |
Woong Jun Kim, Chang Soo Eun, Min Kyu Lee, Seung Yeon Min, Yeon Hwa Yoo, Dong Soo Han, Yong Cheol Jeon, Joo Hyun Sohn |
Department of Internal Medicine, Hanyang University College of Medicine, Seoul, Korea
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성인에서 발생한 후천적 국소 무신경절증 1예 |
김웅준, 은창수, 이민규, 민승연, 유연화, 한동수, 전용철, 손주현 |
한양대학교 의과대학 내과학교실 |
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Abstract |
A chronic intestinal pseudo-obstruction is a rare disorder and a severe digestive syndrome. It is characterized by deranged gut propulsive motility that resembles a mechanical obstruction, but no obstructive process is present. An intestinal pseudo-obstruction may be classified as acute or chronic; the chronic form may also be classified as idiopathic or secondary to a variety of diseases. Treatment of intestinal pseudo-obstruction involves nutritional, pharmacological, and surgical therapies. Surgery should be limited to patients who are refractory to medical therapy and show a deteriorating course. Despite available medical and surgical interventions, the outcome remains poor. Here, we describe a case of a 54-year-old female with chronic constipation and abdominal distension, who was subsequently found to have segmental aganglionosis. The patient was treated with a subtotal colectomy and ileosigmoidostomy without sequelae. (Intest Res 2012;10: 0-214) |
Key Words:
Colonic Pseudo-obstruction, Aganglionosis, Colonic |
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